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Cellular and Clinical Impact of Haploinsufficiency for Genes Involved in ATR Signaling

Ataxia telangiectasia and Rad3-related (ATR) protein, a kinase that regulates a DNA damage–response pathway, is mutated in ATR-Seckel syndrome (ATR-SS), a disorder characterized by severe microcephaly and growth delay. Impaired ATR signaling is also observed in cell lines from additional disorders c...

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Detalhes bibliográficos
Main Authors: O’Driscoll, Mark , Dobyns, William B. , van Hagen, Johanna M. , Jeggo, Penny A. 
Formato: Artigo
Idioma:Inglês
Publicado em: American Society of Human Genetics 2007
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1950915/
https://ncbi.nlm.nih.gov/pubmed/17564965
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