Selective Action of the Iminosugar Isofagomine, a Pharmacological Chaperone For Mutant Forms of Acid-β-Glucosidase

Lignende værker

• The iminosugar isofagomine increases the activity of N370S mutant acid β-glucosidase in Gaucher fibroblasts by several mechanisms
  af: Steet, Richard A., et al.
  Udgivet: (2006)
• The Pharmacological Chaperone Isofagomine Increases Activity of the Gaucher Disease L444P Mutant Form of β-Glucosidase
  af: Khanna, Richie, et al.
  Udgivet: (2010)
• Discovery of a novel non-iminosugar acid alpha glucosidase chaperone series
  af: Xiao, Jingbo, et al.
  Udgivet: (2012)
• The effects of pH and iminosugar pharmacological chaperones on lysosomal glycosidase structure and stability
  af: Lieberman, Raquel L., et al.
  Udgivet: (2009)
• Pharmacological Enhancement of α-Glucosidase by the Allosteric Chaperone N-acetylcysteine
  af: Porto, Caterina, et al.
  Udgivet: (2012)