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Apolipoprotein AI and Transthyretin as Components of Amyloid Fibrils in a Kindred with apoAI Leu178His Amyloidosis

We found a new C-terminal amyloidogenic variant of apolipoprotein AI (apoAI), Leu178His in a French kindred, associated with cardiac and larynx amyloidosis and skin lesions with onset during the fourth decade. This single-point mutation in exon 4 of the apoAI gene was detected by DNA sequencing of p...

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Bibliografski detalji
Glavni autori: de Sousa, Mónica Mendes, Vital, Claude, Ostler, Dominique, Fernandes, Rui, Pouget-Abadie, Jean, Carles, Dominique, Saraiva, Maria João
Format: Artigo
Jezik:Inglês
Izdano: American Society for Investigative Pathology 2000
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC1850097/
https://ncbi.nlm.nih.gov/pubmed/10854214
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