Carregant...

The molecular basis for the two different clinical presentations of classical pyruvate carboxylase deficiency.

Eight cases of isolated human pyruvate carboxylase deficiency were examined from seven families. Although all patients presented with a chronic lacticacidemia, two particular patients presented with the added features of hyperammonemia, citrullinemia, and hyperlysinemia. When cultured skin fibroblas...

Descripció completa

Guardat en:
Dades bibliogràfiques
Autors principals: Robinson, B H, Oei, J, Sherwood, W G, Applegarth, D, Wong, L, Haworth, J, Goodyer, P, Casey, R, Zaleski, L A
Format: Artigo
Idioma:Inglês
Publicat: 1984
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1684418/
https://ncbi.nlm.nih.gov/pubmed/6424438
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!