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Site-specific somatic mitochondrial DNA point mutations in patients with thymidine phosphorylase deficiency

Mitochondrial neurogastrointestinal encephalomyopathy (MNGIE) is an autosomal recessive disorder caused by loss-of-function mutations in the gene encoding thymidine phosphorylase (TP). This deficiency of TP leads to increased circulating levels of thymidine (deoxythymidine, dThd) and deoxyuridine (d...

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Библиографические подробности
Главные авторы: Nishigaki, Yutaka, Martí, Ramon, Copeland, William C., Hirano, Michio
Формат: Artigo
Язык:Inglês
Опубликовано: American Society for Clinical Investigation 2003
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC161426/
https://ncbi.nlm.nih.gov/pubmed/12813027
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI200317828
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