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Peripheral Tissue Involvement in Sporadic, Iatrogenic, and Variant Creutzfeldt-Jakob Disease : An Immunohistochemical, Quantitative, and Biochemical Study

Human prion diseases are rare fatal neurodegenerative conditions that occur as acquired, familial, or idiopathic disorders. A key event in their pathogenesis is the accumulation of an altered form of the prion protein, termed PrP(Sc), in the central nervous system. A novel acquired human prion disea...

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Main Authors: Head, Mark W., Ritchie, Diane, Smith, Nadine, McLoughlin, Victoria, Nailon, William, Samad, Sazia, Masson, Stephen, Bishop, Matthew, McCardle, Linda, Ironside, James W.
Formato: Artigo
Idioma:Inglês
Publicado em: American Society for Investigative Pathology 2004
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1602214/
https://ncbi.nlm.nih.gov/pubmed/14695328
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