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Overexpression of PKD1 Causes Polycystic Kidney Disease

The pathogenetic mechanisms underlying autosomal dominant polycystic kidney disease (ADPKD) remain to be elucidated. While there is evidence that Pkd1 gene haploinsufficiency and loss of heterozygosity can cause cyst formation in mice, paradoxically high levels of Pkd1 expression have been detected...

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Autori principali: Thivierge, Caroline, Kurbegovic, Almira, Couillard, Martin, Guillaume, Richard, Coté, Olivier, Trudel, Marie
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Microbiology 2006
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1367205/
https://ncbi.nlm.nih.gov/pubmed/16449663
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1128/MCB.26.4.1538-1548.2006
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