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Defective insulin receptor activation and altered lipid rafts in Niemann–Pick type C disease hepatocytes

Niemann–Pick type C (NPC) disease is a neuro-visceral cholesterol storage disorder caused by mutations in the NPC-1 or NPC-2 gene. In the present paper, we studied IR (insulin receptor) activation and the plasma-membrane lipid assembly in primary hepatocytes from control and NPC1–/– mice. We have pr...

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Autors principals: Vainio, Saara, Bykov, Igor, Hermansson, Martin, Jokitalo, Eija, Somerharju, Pentti, Ikonen, Elina
Format: Artigo
Idioma:Inglês
Publicat: Portland Press Ltd. 2005
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1276947/
https://ncbi.nlm.nih.gov/pubmed/15943586
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1042/BJ20050460
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