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Reversal of amyloid-induced heart disease in desmin-related cardiomyopathy
Amyloid oligomers, similar to the toxic entities found in Alzheimer's disease patients and in other amyloid-based diseases, are present in cardiomyocytes derived from human heart-failure patients and in animal models of desmin-related cardiomyopathy (DRM). The R120G mutation in α-B-crystallin (...
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| Autores principales: | , , , , , , , |
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| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
National Academy of Sciences
2005
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC1224623/ https://ncbi.nlm.nih.gov/pubmed/16155124 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0503324102 |
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