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Deficiency of α-mannosidase in Angus cattle. An inherited lysosomal storage disease

A disease of Angus cattle previously known as pseudolipidosis has been shown to be an inherited lysosomal storage disease, in which an oligosaccharide containing mannose and glucosamine is the storage substance. Diseased animals have a near-absolute deficiency of the lysosomal enzyme, α-mannosidase,...

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Detaylı Bibliyografya
Asıl Yazarlar: Hocking, J. D., Jolly, R. D., Batt, R. D.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 1972
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC1173571/
https://ncbi.nlm.nih.gov/pubmed/4673577
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