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Characterization of Wild-Type and ΔF508 Cystic Fibrosis Transmembrane Regulator in Human Respiratory Epithelia

Previous studies in native tissues have produced conflicting data on the localization and metabolic fate of WT and ΔF508 cystic fibrosis transmembrane regulator (CFTR) in the lung. Combining immunocytochemical and biochemical studies utilizing new high-affinity CFTR mAbs with ion transport assays, w...

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Autors principals: Kreda, Silvia M., Mall, Marcus, Mengos, April, Rochelle, Lori, Yankaskas, James, Riordan, John R., Boucher, Richard C.
Format: Artigo
Idioma:Inglês
Publicat: The American Society for Cell Biology 2005
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1087225/
https://ncbi.nlm.nih.gov/pubmed/15716351
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1091/mbc.E04-11-1010
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