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Endocytic Trafficking Routes of Wild Type and ΔF508 Cystic Fibrosis Transmembrane Conductance Regulator

Intracellular trafficking of cystic fibrosis transmembrane conductance regulator (CFTR) is a focus of attention because it is defective in most patients with cystic fibrosis. ΔF508 CFTR, which does not mature conformationally, normally does not exit the endoplasmic reticulum, but if induced to do so...

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Autori principali: Gentzsch, Martina, Chang, Xiu-Bao, Cui, Liying, Wu, Yufeng, Ozols, Victor V., Choudhury, Amit, Pagano, Richard E., Riordan, John R.
Natura: Artigo
Lingua:Inglês
Pubblicazione: The American Society for Cell Biology 2004
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC420093/
https://ncbi.nlm.nih.gov/pubmed/15075371
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1091/mbc.E04-03-0176
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