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Dyskeratosis Congenita Associated Non-Specific Interstitial Pneumonia

Dyskeratosis Congenita (DC) is a rare inherited disorder of ectodermal dysplasia. It consists of a classical mucocutaneous triad of abnormal skin pigmentation, nail dystrophy and leukoplakia. Pulmonary disease is seen in 10-15%. It is characterized by Idiopathic Pulmonary Fibrosis (IPF), or Idiopath...

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Autors principals: Unnati D. Desai, Jyotsna M. Joshi
Format: Artigo
Idioma:Inglês
Publicat: Krishna Vishwa Vidyapeeth (Deemed to be University), Karad 2017-01-01
Col·lecció:Journal of Krishna Institute of Medical Sciences University
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Accés en línia:http://www.jkimsu.com/jkimsu-vol6no1/JKIMSU,%20Vol.%206,%20No.%201,%20Jan-Mar%202017%20Page%2099-103.pdf
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