Dyskeratosis Congenita Associated Non-Specific Interstitial Pneumonia
Dyskeratosis Congenita (DC) is a rare inherited disorder of ectodermal dysplasia. It consists of a classical mucocutaneous triad of abnormal skin pigmentation, nail dystrophy and leukoplakia. Pulmonary disease is seen in 10-15%. It is characterized by Idiopathic Pulmonary Fibrosis (IPF), or Idiopath...
Guardat en:
| Autors principals: | , |
|---|---|
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
Krishna Vishwa Vidyapeeth (Deemed to be University), Karad
2017-01-01
|
| Col·lecció: | Journal of Krishna Institute of Medical Sciences University |
| Matèries: | |
| Accés en línia: | http://www.jkimsu.com/jkimsu-vol6no1/JKIMSU,%20Vol.%206,%20No.%201,%20Jan-Mar%202017%20Page%2099-103.pdf |
| Etiquetes: |
Sense etiquetes, Sigues el primer a etiquetar aquest registre!
|
