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Dyskeratosis Congenita Associated Non-Specific Interstitial Pneumonia

Dyskeratosis Congenita (DC) is a rare inherited disorder of ectodermal dysplasia. It consists of a classical mucocutaneous triad of abnormal skin pigmentation, nail dystrophy and leukoplakia. Pulmonary disease is seen in 10-15%. It is characterized by Idiopathic Pulmonary Fibrosis (IPF), or Idiopath...

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Autori principali: Unnati D. Desai, Jyotsna M. Joshi
Natura: Artigo
Lingua:Inglês
Pubblicazione: Krishna Vishwa Vidyapeeth (Deemed to be University), Karad 2017-01-01
Serie:Journal of Krishna Institute of Medical Sciences University
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Accesso online:http://www.jkimsu.com/jkimsu-vol6no1/JKIMSU,%20Vol.%206,%20No.%201,%20Jan-Mar%202017%20Page%2099-103.pdf
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