Diminished Exercise Capacity and Mitochondrial bc1 Complex Deficiency in Tafazzin-Knockdown Mice

di Powers, Corey, Huang, Yan, Strauss, Arnold, Khuchua, Zaza
Pubblicazione 2013

In silico simulation of reversible and irreversible swelling of mitochondria: the role of membrane rigidity

di Makarov, Vladimir I., Khmelinskii, Igor, Khuchua, Zaza, Javadov, Sabzali
Pubblicato in Mitochondrion (2019)

Elucidating the Beneficial Role of PPAR Agonists in Cardiac Diseases

di Khuchua, Zaza, Glukhov, Aleksandr I., Strauss, Arnold W., Javadov, Sabzali
Pubblicato in Int J Mol Sci (2018)

Telomeres and Telomerase in Heart Ontogenesis, Aging and Regeneration

di Nalobin, Denis, Alipkina, Svetlana, Gaidamaka, Anna, Glukhov, Alexander, Khuchua, Zaza
Pubblicato in Cells (2020)

Mitochondrial permeability transition in cardiac ischemia–reperfusion: whether cyclophilin D is a viable target for cardioprotection?

di Javadov, Sabzali, Jang, Sehwan, Parodi-Rullán, Rebecca, Khuchua, Zaza, Kuznetsov, Andrey V.
Pubblicato in Cell Mol Life Sci (2017)

Crosstalk between AMPK activation and angiotensin II-induced hypertrophy in cardiomyocytes: the role of mitochondria

di Hernández, Jessica Soto, Barreto-Torres, Giselle, Kuznetsov, Andrey V, Khuchua, Zaza, Javadov, Sabzali
Pubblicazione 2014

Mitochondrial respiratory supercomplexes in mammalian cells: structural versus functional role

di Javadov, Sabzali, Jang, Sehwan, Chapa-Dubocq, Xavier R., Khuchua, Zaza, Camara, Amadou KS
Pubblicato in J Mol Med (Berl) (2020)

Elucidating Mitochondrial Electron Transport Chain Supercomplexes in the Heart During Ischemia–Reperfusion

di Jang, Sehwan, Lewis, Taber S., Powers, Corey, Khuchua, Zaza, Baines, Christopher P., Wipf, Peter, Javadov, Sabzali
Pubblicato in Antioxid Redox Signal (2017)

Dissection of Z-disc myopalladin gene network involved in the development of restrictive cardiomyopathy using system genetics approach

di Gu, Qingqing, Mendsaikhan, Uzmee, Khuchua, Zaza, Jones, Byron C, Lu, Lu, Towbin, Jeffrey A, Xu, Biao, Purevjav, Enkhsaikhan
Pubblicato in World J Cardiol (2017)

The Effects of PPAR Stimulation on Cardiac Metabolic Pathways in Barth Syndrome Mice

di Schafer, Caitlin, Moore, Vicky, Dasgupta, Nupur, Javadov, Sabzali, James, Jeanne F., Glukhov, Alexander I., Strauss, Arnold W., Khuchua, Zaza
Pubblicato in Front Pharmacol (2018)

Subcellular dynamics of type II PKA in neurons

di Zhong, Haining, Sia, Gek-Ming, Sato, Takashi R., Gray, Noah W., Mao, Tianyi, Khuchua, Zaza, Huganir, Richard L., Svoboda, Karel
Pubblicazione 2009

Distinct Effects of Tafazzin Deletion in Differentiated and Undifferentiated Mitochondria

di Acehan, Devrim, Khuchua, Zaza, Houtkooper, Riekelt H., Malhotra, Ashim, Kaufman, Johanna, Vaz, Frédéric M., Ren, Mindong, Rockman, Howard A., Stokes, David L., Schlame, Michael
Pubblicazione 2008

Cardiac and Skeletal Muscle Defects in a Mouse Model of Human Barth Syndrome

di Acehan, Devrim, Vaz, Frederic, Houtkooper, Riekelt H., James, Jeanne, Moore, Vicky, Tokunaga, Chonan, Kulik, Willem, Wansapura, Janaka, Toth, Matthew J., Strauss, Arnold, Khuchua, Zaza
Pubblicazione 2011

Creatine transporter deficiency leads to increased whole-body and cellular metabolism

di Perna, Marla K., Kokenge, Amanda N., Miles, Keila N., Udobi, Kenea C., Clark, Joseph F., Pyne-Geithman, Gail J., Khuchua, Zaza, Skelton, Matthew R.
Pubblicato in Amino Acids (2016)

Cardiac Metabolic Pathways Affected in the Mouse Model of Barth Syndrome

di Huang, Yan, Powers, Corey, Madala, Satish K., Greis, Kenneth D., Haffey, Wendy D., Towbin, Jeffrey A., Purevjav, Enkhsaikhan, Javadov, Sabzali, Strauss, Arnold W., Khuchua, Zaza
Pubblicato in PLoS One (2015)

Single Amino Acid Substitution in Aquaporin 11 Causes Renal Failure

di Tchekneva, Elena E., Khuchua, Zaza, Davis, Linda S., Kadkina, Veronika, Dunn, Stephen R., Bachman, Sebastian, Ishibashi, Kenichi, Rinchik, Eugene M., Harris, Raymond C., Dikov, Mikhail M., Breyer, Matthew D.
Pubblicazione 2008

Deficiency in nebulin repeats of sarcomeric nebulette is detrimental for cardiomyocyte tolerance to exercise and biomechanical stress

di Vejandla, Ramona M., Orgil, Buyan-Ochir, Alberson, Neely R., Li, Ning, Munkhsaikhan, Undral, Khuchua, Zaza, Martherus, Ruben, Azeloglu, Evren U., Xu, Fuyi, Lu, Lu, Towbin, Jeffrey A., Purevjav, Enkhsaikhan
Pubblicato in Am J Physiol Heart Circ Physiol (2021)

Disturbance in Z-disk mechanosensitive proteins induced by a persistent mutant myopalladin causes familial restrictive cardiomyopathy

di Huby, Anne-Cecile, Mendsaikhan, Uzmee, Takagi, Ken, Martherus, Ruben, Wansapura, Janaka, Gong, Nan, Osinska, Hanna, James, Jeanne, Kramer, Kristen, Saito, Kazuyoshi, Robbins, Jeffrey, Khuchua, Zaza, Towbin, Jeffrey A., Purevjav, Enkhsaikhan
Pubblicato in J Am Coll Cardiol (2014)

Cardiac-specific VLCAD deficiency induces dilated cardiomyopathy and cold intolerance

di Xiong, Dingding, He, Huamei, James, Jeanne, Tokunaga, Chonan, Powers, Corey, Huang, Yan, Osinska, Hanna, Towbin, Jeffrey A., Purevjav, Enkhsaikhan, Balschi, James A., Javadov, Sabzali, McGowan, Francis X., Strauss, Arnold W., Khuchua, Zaza
Pubblicazione 2013

The PPAR pan-agonist bezafibrate ameliorates cardiomyopathy in a mouse model of Barth syndrome

di Huang, Yan, Powers, Corey, Moore, Victoria, Schafer, Caitlin, Ren, Mindong, Phoon, Colin K. L., James, Jeanne F., Glukhov, Alexander V., Javadov, Sabzali, Vaz, Frédéric M., Jefferies, John L., Strauss, Arnold W., Khuchua, Zaza
Pubblicato in Orphanet J Rare Dis (2017)