Redecorating the Mitochondrial Inner Membrane: A Treatment for mtDNA Disorders

di Chrzanowska-Lightowlers, Zofia M.A., Lightowlers, Robert N.
Pubblicato in Mol Ther (2020)

Fine mapping of interactions between eEF1α protein and 3′UTR of metallothionein-1 mRNA

di Fan, Kunbo, Chrzanowska-Lightowlers, Zofia M.A., Hesketh, John E.
Pubblicazione 2009

Termination of Protein Synthesis in Mammalian Mitochondria

di Chrzanowska-Lightowlers, Zofia M. A., Pajak, Aleksandra, Lightowlers, Robert N.
Pubblicazione 2011

The process of mammalian mitochondrial protein synthesis

di Mai, Nicole, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N.
Pubblicato in Cell Tissue Res (2016)

Structure based hypothesis of a mitochondrial ribosome rescue mechanism

di Huynen, Martijn A, Duarte, Isabel, Chrzanowska-Lightowlers, Zofia M A, Nabuurs, Sander B
Pubblicazione 2012

Overcoming stalled translation in human mitochondria

di Wesolowska, Maria T., Richter-Dennerlein, Ricarda, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A.
Pubblicazione 2014

Serum-deprivation stimulates cap-binding by PARN at the expense of eIF4E, consistent with the observed decrease in mRNA stability

di Seal, Ruth, Temperley, Richard, Wilusz, Jeffrey, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A.
Pubblicazione 2005

Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

di Dennerlein, Sven, Rozanska, Agata, Wydro, Mateusz, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N.
Pubblicazione 2010

REXO2 Is an Oligoribonuclease Active in Human Mitochondria

di Bruni, Francesco, Gramegna, Pasqua, Oliveira, Jorge M. A., Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A.
Pubblicazione 2013

High-resolution imaging reveals compartmentalization of mitochondrial protein synthesis in cultured human cells

di Zorkau, Matthew, Albus, Christin A., Berlinguer-Palmini, Rolando, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N.
Pubblicato in Proc Natl Acad Sci U S A (2021)

Functional polypeptides can be synthesized from human mitochondrial transcripts lacking termination codons.

di Chrzanowska-Lightowlers, Zofia M A, Temperley, Richard J, Smith, Paul M, Seneca, Sara H, Lightowlers, Robert N
Pubblicazione 2004

Sodium Channel mRNAs at the Neuromuscular Junction: Distinct Patterns of Accumulation and Effects of Muscle Activity

di Awad, Suad S., Lightowlers, Robert N., Young, Carol, Chrzanowska-Lightowlers, Zofia M. A., Lømo, Terje, Slater, Clarke R.
Pubblicato in J Neurosci (2001)

SLIRP stabilizes LRPPRC via an RRM–PPR protein interface

di Spåhr, Henrik, Rozanska, Agata, Li, Xinping, Atanassov, Ilian, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A., Rackham, Oliver, Larsson, Nils-Göran
Pubblicato in Nucleic Acids Res (2016)

Using mitoribosomal profiling to investigate human mitochondrial translation

di Gao, Fei, Wesolowska, Maria, Agami, Reuven, Rooijers, Koos, Loayza-Puch, Fabricio, Lawless, Conor, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A.
Pubblicato in Wellcome Open Res (2018)

The presence of highly disruptive 16S rRNA mutations in clinical samples indicates a wider role for mutations of the mitochondrial ribosome in human disease

di Elson, Joanna L., Smith, Paul M., Greaves, Laura C., Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M.A., Taylor, Robert W., Vila-Sanjurjo, Antón
Pubblicato in Mitochondrion (2015)

Production of transmitochondrial cybrids containing naturally occurring pathogenic mtDNA variants

di Pye, Deborah, Kyriakouli, Dimitra S., Taylor, Geoffrey A., Johnson, Riem, Elstner, Matthias, Meunier, Brigitte, Chrzanowska-Lightowlers, Zofia M. A., Taylor, Robert W., Turnbull, Douglass M., Lightowlers, Robert N.
Pubblicazione 2006

Overexpression of human mitochondrial valyl tRNA synthetase can partially restore levels of cognate mt-tRNA(Val) carrying the pathogenic C25U mutation

di Rorbach, Joanna, Yusoff, Abdul Aziz, Tuppen, Helen, Abg-Kamaludin, Dyg P., Chrzanowska-Lightowlers, Zofia M.A., Taylor, Robert W., Turnbull, Douglass M., McFarland, Robert, Lightowlers, Robert N.
Pubblicazione 2008

The role of the mitochondrial ribosome in human disease: searching for mutations in 12S mitochondrial rRNA with high disruptive potential

di Smith, Paul M., Elson, Joanna L., Greaves, Laura C., Wortmann, Saskia B., Rodenburg, Richard J.T., Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M.A., Taylor, Robert W., Vila-Sanjurjo, Antón
Pubblicazione 2014

The human mitochondrial ribosome recycling factor is essential for cell viability

di Rorbach, Joanna, Richter, Ricarda, Wessels, Hans J., Wydro, Mateusz, Pekalski, Marcin, Farhoud, Murtada, Kühl, Inge, Gaisne, Mauricette, Bonnefoy, Nathalie, Smeitink, Jan A., Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M.A.
Pubblicazione 2008

Defective mitochondrial protease LonP1 can cause classical mitochondrial disease

di Peter, Bradley, Waddington, Christie L, Oláhová, Monika, Sommerville, Ewen W, Hopton, Sila, Pyle, Angela, Champion, Michael, Ohlson, Monica, Siibak, Triinu, Chrzanowska-Lightowlers, Zofia M A, Taylor, Robert W, Falkenberg, Maria, Lightowlers, Robert N
Pubblicato in Hum Mol Genet (2018)