Experimental animal model for mucopolysaccharidosis: suramin-induced glycosaminoglycan and sphingolipid accumulation in the rat.

Por Constantopoulos, G, Rees, S, Cragg, B G, Barranger, J A, Brady, R O
Publicado em 1980

Suramin-induced storage disease. Mucopolysaccharidosis.

Por Constantopoulos, G., Rees, S., Cragg, B. G., Barranger, J. A., Brady, R. O.
Publicado em 1983

Identification of the binding and activating sites of the sphingolipid activator protein, saposin C, with glucocerebrosidase.

Por Weiler, S., Kishimoto, Y., O'Brien, J. S., Barranger, J. A., Tomich, J. M.
Publicado em 1995

Genetic heterogeneity in type 1 Gaucher disease: multiple genotypes in Ashkenazic and non-Ashkenazic individuals.

Por Tsuji, S, Martin, B M, Barranger, J A, Stubblefield, B K, LaMarca, M E, Ginns, E I
Publicado em 1988

Gene mapping and leader polypeptide sequence of human glucocerebrosidase: implications for Gaucher disease.

Por Ginns, E I, Choudary, P V, Tsuji, S, Martin, B, Stubblefield, B, Sawyer, J, Hozier, J, Barranger, J A
Publicado em 1985

Role of pH in determining the cell-type-specific residual activity of glucocerebrosidase in type 1 Gaucher disease.

Por van Weely, S, van den Berg, M, Barranger, J A, Sa Miranda, M C, Tager, J M, Aerts, J M
Publicado em 1993

Mutations of glucocerebrosidase: discrimination of neurologic and non-neurologic phenotypes of Gaucher disease.

Por Ginns, E I, Brady, R O, Pirruccello, S, Moore, C, Sorrell, S, Furbish, F S, Murray, G J, Tager, J, Barranger, J A
Publicado em 1982

Delivery of hexosaminidase A to the cerebrum after osmotic modification of the blood--brain barrier.

Por Neuwelt, E A, Barranger, J A, Brady, R O, Pagel, M, Furbish, F S, Quirk, J M, Mook, G E, Frenkel, E
Publicado em 1981

Modification of the blood-brain barrier: increased concentration and fate of enzymes entering the brain.

Por Barranger, J A, Rapoport, S I, Fredericks, W R, Pentchev, P G, MacDermot, K D, Steusing, J K, Brady, R O
Publicado em 1979

Comparative study on glucocerebrosidase in spleens from patients with Gaucher disease.

Por Aerts, J M, Donker-Koopman, W E, Brul, S, Van Weely, S, Sa Miranda, M C, Barranger, J A, Tager, J M, Schram, A W
Publicado em 1990