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A human monoclonal antibody against the distal carboxyl terminus of ADAMTS13 modulates its susceptibility to an inhibitor in thrombotic thrombocytopenic purpura

BACKGROUND: Immune thrombotic thrombocytopenic purpura (iTTP) is a potentially fatal thrombotic microangiopathy, resulting from a severe deficiency of plasma ADAMTS13 activity. Immunoglobulin (Ig) G-type autoantibodies are primarily responsible for the inhibition of plasma ADAMTS13 activity. However...

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Библиографические подробности
Опубликовано в: :J Thromb Haemost
Главные авторы: Halkidis, Konstantine, Siegel, Don L., Zheng, X. Long
Формат: Artigo
Язык:Inglês
Опубликовано: 2021
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC8324539/
https://ncbi.nlm.nih.gov/pubmed/33834592
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/jth.15332
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