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Skeletal Muscle Mitochondria Dysfunction in Genetic Neuromuscular Disorders with Cardiac Phenotype

Mitochondrial dysfunction is considered the major contributor to skeletal muscle wasting in different conditions. Genetically determined neuromuscular disorders occur as a result of mutations in the structural proteins of striated muscle cells and therefore are often combined with cardiac phenotype,...

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Bibliografiske detaljer
Udgivet i:Int J Mol Sci
Main Authors: Ignatieva, Elena, Smolina, Natalia, Kostareva, Anna, Dmitrieva, Renata
Format: Artigo
Sprog:Inglês
Udgivet: MDPI 2021
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC8307986/
https://ncbi.nlm.nih.gov/pubmed/34298968
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms22147349
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