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Activated PI3Kinase Delta Syndrome—A Multifaceted Disease

Autosomal dominant gain-of-function mutations in the PIK3CD gene encoding the catalytic subunit p110δ of phosphoinositide 3-kinase-δ (PI3K-δ) or autosomal dominant loss-of-function mutations in the PIK3R1 gene encoding the p85α, p55α and p50α regulatory subunits cause Activated PI3-kinase-δ syndrome...

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Dades bibliogràfiques
Publicat a:Front Pediatr
Autors principals: Thouenon, Romane, Moreno-Corona, Nidia, Poggi, Lucie, Durandy, Anne, Kracker, Sven
Format: Artigo
Idioma:Inglês
Publicat: Frontiers Media S.A. 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8267809/
https://ncbi.nlm.nih.gov/pubmed/34249806
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fped.2021.652405
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