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Novel folliculin gene mutations in Polish patients with Birt–Hogg–Dubé syndrome

BACKGROUND: Birt–Hogg–Dubé syndrome (BHDS) is a rare, autosomal dominant, inherited disease caused by mutations in the folliculin gene (FLCN). The disease is characterised by skin lesions (fibrofolliculomas, trichodiscomas, acrochordons), pulmonary cysts with pneumothoraces and renal tumours. We pre...

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Detaylı Bibliyografya
Yayımlandı:Orphanet J Rare Dis
Asıl Yazarlar: Radzikowska, Elżbieta, Lechowicz, Urszula, Winek, Jolanta, Opoka, Lucyna
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: BioMed Central 2021
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC8258955/
https://ncbi.nlm.nih.gov/pubmed/34229741
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-021-01931-0
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