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Muscle Fiber Conduction Velocity Correlates With the Age at Onset in Mild FSHD Cases

A majority of patients with facioscapulohumeral muscular dystrophy (FSHD) report severe fatigue. The aim of this study was to explore whether fatigability during a performance task is related to the main clinical features of the disease in mildly affected patients. A total of 19 individuals with a m...

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Publicat a:Front Physiol
Autors principals: Beretta-Piccoli, Matteo, Negro, Massimo, Calanni, Luca, Berardinelli, Angela, Siciliano, Gabriele, Tupler, Rossella, Soldini, Emiliano, Cescon, Corrado, D’Antona, Giuseppe
Format: Artigo
Idioma:Inglês
Publicat: Frontiers Media S.A. 2021
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8247588/
https://ncbi.nlm.nih.gov/pubmed/34220550
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphys.2021.686176
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