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Cardiolipin remodeling defects impair mitochondrial architecture and function in a murine model of Barth syndrome cardiomyopathy

BACKGROUND: Cardiomyopathy is a major clinical feature in Barth syndrome (BTHS), an X-linked mitochondrial lipid disorder caused by mutations in Tafazzin (TAZ), encoding a mitochondrial acyltransferase required for cardiolipin (CL) remodeling. Despite recent description of a mouse model of BTHS card...

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מידע ביבליוגרפי
הוצא לאור ב:	Circ Heart Fail
Main Authors:	Zhu, Siting, Chen, Ze’e, Zhu, Mason, Shen, Ying, Leon, Leonardo J, Chi, Liguo, Spinozzi, Simone, Tan, Changming, Gu, Yusu, Nguyen, Anh, Zhou, Yi, Feng, Wei, Vaz, Frédéric M, Wang, Xiaohong, Gustafsson, Asa B, Evans, Sylvia M, Kunfu, Ouyang, Fang, Xi
פורמט:	Artigo
שפה:	Inglês
יצא לאור:	2021
נושאים:	Article
גישה מקוונת:	https://ncbi.nlm.nih.gov/pmc/articles/PMC8210459/ https://ncbi.nlm.nih.gov/pubmed/34129362 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCHEARTFAILURE.121.008289
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Cardiolipin remodeling defects impair mitochondrial architecture and function in a murine model of Barth syndrome cardiomyopathy

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