Caricamento...

Hepatic and Extrahepatic Sources and Manifestations in Endoplasmic Reticulum Storage Diseases

Alpha-1-antitrypsin (AAT) and fibrinogen are secretory acute phase reactant proteins. Circulating AAT and fibrinogen are synthesized exclusively in the liver. Mutations in the encoding genes result in conformational abnormalities of the two molecules that aggregate within the rough endoplasmic retic...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Int J Mol Sci
Autori principali: Callea, Francesco, Francalanci, Paola, Giovannoni, Isabella
Natura: Artigo
Lingua:Inglês
Pubblicazione: MDPI 2021
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8198767/
https://ncbi.nlm.nih.gov/pubmed/34071368
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms22115778
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !