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A Rare and Misdiagnosed Entity Paroxysmal Nocturnal Hemoglobinuria: A Case Report

Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, acquired stem cell disorder manifesting as non-immunological hemolytic anemia, hemoglobinuria, unusual thrombosis, and renal impairment due to deficiency of glycosylphosphatidylinositol (GPI) linked proteins in red blood cells. Patients present wi...

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Dades bibliogràfiques
Publicat a:Cureus
Autors principals: Pokhrel, Biraj, Gautam, Sandesh, Khanal, Shambhu, Pokhrel, Nishan B, Shrestha, Anjan
Format: Artigo
Idioma:Inglês
Publicat: Cureus 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8183308/
https://ncbi.nlm.nih.gov/pubmed/34109088
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7759/cureus.14902
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