A carregar...

Lipid-mediated motor-adaptor sequestration impairs axonal lysosome delivery leading to autophagic stress and dystrophy in Niemann-Pick type C

Niemann-Pick disease type C (NPC) is a neurodegenerative lysosomal storage disorder characterized by lipid accumulation in endolysosomes. An early pathologic hallmark is axonal dystrophy occurring at presymptomatic stages in NPC mice. However, the mechanisms underlying this pathologic change remain...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Dev Cell
Main Authors: Roney, Joseph C, Li, Sunan, Farfel-Becker, Tamar, Huang, Ning, Sun, Tao, Xie, Yuxiang, Cheng, Xiu-Tang, Lin, Mei-Yao, Platt, Frances M, Sheng, Zu-Hang
Formato: Artigo
Idioma:Inglês
Publicado em: 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8137671/
https://ncbi.nlm.nih.gov/pubmed/33878344
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.devcel.2021.03.032
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!