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Heterozygous Recurrent HNF4A variant p.Arg85Trp Causes Fanconi Renotubular Syndrome 4 with Maturity Onset Diabetes of the Young, an Autosomal Dominant Phenocopy of Fanconi Bickel Syndrome with Colobomas

Heterozygous pathogenic variants in HNF4A cause hyperinsulinism, maturity onset diabetes of the young type 1, and more rarely Fanconi renotubular syndrome. Specifically, the recurrent point pathogenic variant c.253C >T (p.Arg85Trp) has been associated with a syndromic form of hyperinsulinism with...

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Detalhes bibliográficos
Publicado no:Am J Med Genet A
Main Authors: Sheppard, Sarah E., Barrett, Brett, Muraresku, Colleen, McKnight, Heather, De Leon, Diva D., Lord, Katherine, Ganetzky, Rebecca
Formato: Artigo
Idioma:Inglês
Publicado em: 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8132289/
https://ncbi.nlm.nih.gov/pubmed/33251707
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajmg.a.61978
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