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Exacerbations of Lung Disease in Alpha-1 Antitrypsin Deficiency

Alpha-1 antitrypsin deficiency (AATD) is an important risk factor for development of chronic obstructive pulmonary disease (COPD). Patients with AATD classically develop a different pattern of lung disease from those with usual COPD, decline faster and exhibit a range of differences in pathogenesis,...

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Pubblicato in:Chronic Obstr Pulm Dis
Autori principali: Smith, Daniel J., Ellis, Paul R., Turner, Alice M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: COPD Foundation Inc 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8047608/
https://ncbi.nlm.nih.gov/pubmed/33238089
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.15326/jcopdf.2020.0173
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