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Treatment of lung disease in alpha-1 antitrypsin deficiency: a systematic review

BACKGROUND: Alpha-1 antitrypsin deficiency (AATD) is a rare genetic condition predisposing individuals to chronic obstructive pulmonary disease (COPD). The treatment is generally extrapolated from COPD unrelated to AATD; however, most COPD trials exclude AATD patients; thus, this study sought to sys...

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Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Int J Chron Obstruct Pulmon Dis
Egile Nagusiak: Edgar, Ross G, Patel, Mitesh, Bayliss, Susan, Crossley, Diana, Sapey, Elizabeth, Turner, Alice M
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Dove Medical Press 2017
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC5422329/
https://ncbi.nlm.nih.gov/pubmed/28496314
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2147/COPD.S130440
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