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Interstitial Pneumonia Secondary to Hermansky-Pudlak Syndrome Type 4 Treated with Different Antifibrotic Agents

Hermansky-Pudlak syndrome (HPS) is an autosomal recessive hereditary disease that may be complicated by progressive and potentially fatal interstitial pneumonia. We herein report a 64-year-old woman with interstitial pneumonia associated with HPS type 4 whom we treated with nintedanib after pirfenid...

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Bibliografiska uppgifter
I publikationen:Intern Med
Huvudupphovsmän: Itano, Junko, Tanimoto, Yasushi, Kimura, Goro, Hamada, Noboru, Tanaka, Hisaaki, Ninomiya, Shinsuke, Kosaki, Kenjiro, Miyahara, Nobuaki, Maeda, Yoshinobu, Kiura, Katsuyuki
Materialtyp: Artigo
Språk:Inglês
Publicerad: The Japanese Society of Internal Medicine 2020
Ämnen:
Länkar:https://ncbi.nlm.nih.gov/pmc/articles/PMC7990633/
https://ncbi.nlm.nih.gov/pubmed/33229802
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2169/internalmedicine.5493-20
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