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Deterioration of pulmonary function: An early complication in Fibrodysplasia Ossificans Progressiva

Fibrodysplasia Ossificans Progressiva (FOP) is a genetic disease characterized by the formation of heterotopic ossification (HO) in connective tissues. HO first develops in the thoracic region, before more peripheral sites are affected. Due to HO along the thoracic cage, its movements are restricted...

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Библиографические подробности
Опубликовано в: :Bone Rep
Главные авторы: Botman, Esmée, Smilde, Bernard J., Hoebink, Max, Treurniet, Sanne, Raijmakers, Pieter, Kamp, Otto, Teunissen, Bernd P., Bökenkamp, Arend, Jak, Patrick, Lammertsma, Adriaan A., van den Aardweg, Joost G., Boonstra, Anco, Eekhoff, Elisabeth M.W.
Формат: Artigo
Язык:Inglês
Опубликовано: Elsevier 2021
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC7972965/
https://ncbi.nlm.nih.gov/pubmed/33748352
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bonr.2021.100758
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