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IPEX Syndrome: Improved Knowledge of Immune Pathogenesis Empowers Diagnosis

Immune dysregulation, polyendocrinopathy, enteropathy, X-linked (IPEX) syndrome is a rare monogenic autoimmune disease with variable clinical manifestations, ranging from early-onset severe autoimmunity, including enteropathy, eczema, and type 1 diabetes, to late-onset or atypical symptoms. Despite...

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Detalles Bibliográficos
Publicado en:Front Pediatr
Main Authors: Barzaghi, Federica, Passerini, Laura
Formato: Artigo
Idioma:Inglês
Publicado: Frontiers Media S.A. 2021
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7937806/
https://ncbi.nlm.nih.gov/pubmed/33692972
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fped.2021.612760
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