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B cell‐activating factors in autoimmune pulmonary alveolar proteinosis
BACKGROUND: Autoimmune pulmonary alveolar proteinosis (APAP) results from the suppression of granulocyte-macrophage colony-stimulating factor (GM-CSF) signaling by a neutralizing autoantibody against GM-CSF. B cell-activating factor (BAFF) and a proliferation-inducing ligand (APRIL) are involved in...
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| Publicat a: | Orphanet J Rare Dis |
|---|---|
| Autors principals: | , , , , , , , , , , , , , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
BioMed Central
2021
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7923513/ https://ncbi.nlm.nih.gov/pubmed/33653382 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-021-01755-y |
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