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B cell‐activating factors in autoimmune pulmonary alveolar proteinosis

BACKGROUND: Autoimmune pulmonary alveolar proteinosis (APAP) results from the suppression of granulocyte-macrophage colony-stimulating factor (GM-CSF) signaling by a neutralizing autoantibody against GM-CSF. B cell-activating factor (BAFF) and a proliferation-inducing ligand (APRIL) are involved in...

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Detalhes bibliográficos
Publicado no:Orphanet J Rare Dis
Main Authors: Hirose, Masaki, Arai, Toru, Sugimoto, Chikatoshi, Takimoto, Takayuki, Sugawara, Reiko, Minomo, Shojiro, Shintani, Sayoko, Takeuchi, Naoko, Katayama, Kanako, Inoue, Yasushi, Kagawa, Tomoko, Kasai, Takahiko, Akira, Masanori, Inoue, Yoshikazu
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7923513/
https://ncbi.nlm.nih.gov/pubmed/33653382
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-021-01755-y
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