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Loss of COX4I1 Leads to Combined Respiratory Chain Deficiency and Impaired Mitochondrial Protein Synthesis

The oxidative phosphorylation (OXPHOS) system localized in the inner mitochondrial membrane secures production of the majority of ATP in mammalian organisms. Individual OXPHOS complexes form supramolecular assemblies termed supercomplexes. The complexes are linked not only by their function but also...

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Publicat a:Cells
Autors principals: Čunátová, Kristýna, Reguera, David Pajuelo, Vrbacký, Marek, Fernández-Vizarra, Erika, Ding, Shujing, Fearnley, Ian M., Zeviani, Massimo, Houštěk, Josef, Mráček, Tomáš, Pecina, Petr
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7916595/
https://ncbi.nlm.nih.gov/pubmed/33578848
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/cells10020369
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