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Continuous use of glycomacropeptide in the nutritional management of patients with phenylketonuria: a clinical perspective

BACKGROUND: In phenylketonuria (PKU), modified casein glycomacropeptide supplements (CGMP-AA) are used as an alternative to the traditional phenylalanine (Phe)-free L-amino acid supplements (L-AA). However, studies focusing on the long-term nutritional status of CGMP-AA are lacking. This retrospecti...

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Détails bibliographiques
Publié dans:Orphanet J Rare Dis
Auteurs principaux: Pena, Maria João, Pinto, Alex, de Almeida, Manuela Ferreira, de Sousa Barbosa, Catarina, Ramos, Paula Cristina, Rocha, Sara, Guimas, Arlindo, Ribeiro, Rosa, Martins, Esmeralda, Bandeira, Anabela, Dias, Cláudia Camila, MacDonald, Anita, Borges, Nuno, Rocha, Júlio César
Format: Artigo
Langue:Inglês
Publié: BioMed Central 2021
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7881530/
https://ncbi.nlm.nih.gov/pubmed/33581730
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-021-01721-8
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