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Wolman’s disease presenting with secondary hemophagocytic lymphohistiocytosis: a case report from Saudi Arabia and literature review

BACKGROUND: Hemophagocytic lymphohistiocytosis (HLH) is a rare and potentially fatal syndrome that is characterized by strong activation of the immune system from hyperinflammatory cytokines. Symptoms of HLH patients include fever, hepatosplenomegaly, cytopenia, and hyperferritinemia. Inherited HLH...

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Dades bibliogràfiques
Publicat a:BMC Pediatr
Autors principals: Alabbas, Fahad, Elyamany, Ghaleb, Alanzi, Talal, Ali, Tahani Bin, Albatniji, Fatma, Alfaraidi, Huda
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7874635/
https://ncbi.nlm.nih.gov/pubmed/33568092
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12887-021-02541-2
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