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Thrombotic Thrombocytopenic Purpura: Pathophysiology, Diagnosis, and Management

Thrombotic thrombocytopenic purpura (TTP) is a rare thrombotic microangiopathy characterized by microangiopathic hemolytic anemia, severe thrombocytopenia, and ischemic end organ injury due to microvascular platelet-rich thrombi. TTP results from a severe deficiency of the specific von Willebrand fa...

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Dades bibliogràfiques
Publicat a:J Clin Med
Autors principals: Sukumar, Senthil, Lämmle, Bernhard, Cataland, Spero R.
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7867179/
https://ncbi.nlm.nih.gov/pubmed/33540569
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/jcm10030536
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