Lanean...

A Rare Case of Ataxia-Telangiectasia-Like Disorder With MRE11 Mutation

The prototypical disorder for the early-onset cerebellar ataxia with cerebellar atrophy is ataxia telangiectasia (AT). AT belongs to “DNA-repair defects” or “DNA-repair deficiency” disorders. The ATM (Ataxia-telangiectasia mutated kinase) gene mutated in AT is central to deoxyribonucleic acid (DNA)...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:J Pediatr Neurosci
Egile Nagusiak: Mahale, Rohan R, Reddy, Nishanth, Mathuranth, Pavagada, Mailankody, Pooja, Padmanabha, Hansashree, Retnaswami, Chandra Sadnavalli
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Wolters Kluwer - Medknow 2020
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC7847126/
https://ncbi.nlm.nih.gov/pubmed/33531947
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/jpn.JPN_152_19
Etiketak: Etiketa erantsi
Etiketarik gabe, Izan zaitez lehena erregistro honi etiketa jartzen!