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Cardiomyopathic troponin mutations predominantly occur at its interface with actin and tropomyosin

Reversible Ca(2+) binding to troponin is the primary on-off switch of the contractile apparatus of striated muscles, including the heart. Dominant missense mutations in human cardiac troponin genes are among the causes of hypertrophic cardiomyopathy (HCM) and dilated cardiomyopathy. Structural under...

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Pubblicato in:J Gen Physiol
Autori principali: Tobacman, Larry S., Cammarato, Anthony
Natura: Artigo
Lingua:Inglês
Pubblicazione: Rockefeller University Press 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7836260/
https://ncbi.nlm.nih.gov/pubmed/33492345
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1085/jgp.202012815
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