Caricamento...

Nuclear Pore Complexes Cluster in Dysmorphic Nuclei of Normal and Progeria Cells during Replicative Senescence

Hutchinson-Gilford progeria syndrome (HGPS) is a rare premature aging disease caused by a mutation in LMNA. A G608G mutation in exon 11 of LMNA is responsible for most HGPS cases, generating a truncated protein called “progerin”. Progerin is permanently farnesylated and accumulates in HGPS cells, ca...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Cells
Autori principali: Röhrl, Jennifer M., Arnold, Rouven, Djabali, Karima
Natura: Artigo
Lingua:Inglês
Pubblicazione: MDPI 2021
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7828780/
https://ncbi.nlm.nih.gov/pubmed/33466669
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/cells10010153
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !