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Functional Evaluation of a Rare Variant c.516G>C (p.Trp172Cys) in the GJB2 (Connexin 26) Gene Associated with Nonsyndromic Hearing Loss

Mutations in the GJB2 gene encoding transmembrane protein connexin 26 (Cx26) are the most common cause for hearing loss worldwide. Cx26 plays a crucial role in the ionic and metabolic homeostasis in the inner ear, indispensable for normal hearing process. Different pathogenic mutations in the GJB2 g...

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Publicat a:Biomolecules
Autors principals: Maslova, Ekaterina A., Orishchenko, Konstantin E., Posukh, Olga L.
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7824951/
https://ncbi.nlm.nih.gov/pubmed/33466560
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/biom11010061
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