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Mast cell inhibition as a therapeutic approach in fibrodysplasia ossificans progressiva (FOP)

BACKGROUND: Episodic flare-ups of fibrodysplasia ossificans progressiva (FOP) are characterized clinically by severe, often posttraumatic, connective tissue swelling and intramuscular edema, followed histologically by an intense and highly angiogenic fibroproliferative reaction. This early inflammat...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:Bone
Päätekijät: Brennan, Tracy A., Lindborg, Carter M., Bergbauer, Christian R., Wang, Haitao, Kaplan, Frederick S., Pignolo, Robert J.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2017
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC7805128/
https://ncbi.nlm.nih.gov/pubmed/28851540
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bone.2017.08.023
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