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Fibrodysplasia Ossificans Progressiva (FOP): A Disorder of Osteochondrogenesis
Fibrodysplasia Ossificans Progressiva (FOP) is an ultra-rare genetic disorder of extraskeletal bone formation, but could appropriately be viewed as a seminal disorder of osteochondrogenesis. Many, if not most, of the musculoskeletal features of FOP are related to dysregulated chondrogenesis includin...
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| Publicado en: | Bone |
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| Autores principales: | , , , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
2020
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7502483/ https://ncbi.nlm.nih.gov/pubmed/32730934 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bone.2020.115539 |
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