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CEP290 is essential for the initiation of ciliary transition zone assembly

Cilia play critical roles during embryonic development and adult homeostasis. Dysfunction of cilia leads to various human genetic diseases, including many caused by defects in transition zones (TZs), the “gates” of cilia. The evolutionarily conserved TZ component centrosomal protein 290 (CEP290) is...

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Dades bibliogràfiques
Publicat a:PLoS Biol
Autors principals: Wu, Zhimao, Pang, Nan, Zhang, Yingying, Chen, Huicheng, Peng, Ying, Fu, Jingyan, Wei, Qing
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7793253/
https://ncbi.nlm.nih.gov/pubmed/33370260
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pbio.3001034
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