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Bone marrow necrosis and fat embolism syndrome: a near fatal complication in previously undiagnosed sickle beta + thalassaemia
Prevalence of haemoglobin sickle-β(+) thalassaemia (Hb S/β+thal) is variable with geography ranging from 0.2% to 10% among sickle cell patients. Clinical presentation of Hb S/β+thal patients depends on HbA level, with milder disease often going undiagnosed. However, rarely these patients can present...
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| Опубликовано в: : | BMJ Case Rep |
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| Главные авторы: | , , , |
| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
BMJ Publishing Group
2021
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| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7789434/ https://ncbi.nlm.nih.gov/pubmed/33408108 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2020-238317 |
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