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Bone marrow necrosis and fat embolism syndrome: a near fatal complication in previously undiagnosed sickle beta + thalassaemia

Prevalence of haemoglobin sickle-β(+) thalassaemia (Hb S/β+thal) is variable with geography ranging from 0.2% to 10% among sickle cell patients. Clinical presentation of Hb S/β+thal patients depends on HbA level, with milder disease often going undiagnosed. However, rarely these patients can present...

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Detalhes bibliográficos
Publicado no:BMJ Case Rep
Main Authors: Budhathoki, Nibash, Timilsina, Sunita, Ram, Bebu, Marks, Douglas
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2021
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7789434/
https://ncbi.nlm.nih.gov/pubmed/33408108
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2020-238317
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