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Predictors of mortality in patients with hereditary hemorrhagic telangiectasia

BACKGROUND: Retrospective questionnaire and healthcare administrative data suggest reduced life expectancy in untreated hereditary hemorrhagic telangiectasia (HHT). Prospective data suggests similar mortality, to the general population, in Denmark’s centre-treated HHT patients. However, clinical phe...

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Pubblicato in:Orphanet J Rare Dis
Autori principali: Thompson, K. P., Nelson, J., Kim, H., Pawlikowska, L., Marchuk, D. A., Lawton, M. T., Faughnan, Marie E.
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7789194/
https://ncbi.nlm.nih.gov/pubmed/33407668
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-020-01579-2
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