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What Works When Treating Granulomatous Disease in Genetically Undefined CVID? A Systematic Review

BACKGROUND: Granulomatous disease is reported in at least 8–20% of patients with common variable immunodeficiency (CVID). Granulomatous disease mainly affects the lungs, and is associated with significantly higher morbidity and mortality. In half of patients with granulomatous disease, extrapulmonar...

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Detalhes bibliográficos
Publicado no:Front Immunol
Main Authors: van Stigt, Astrid C., Dik, Willem A., Kamphuis, Lieke S. J., Smits, Bas M., van Montfrans, Joris M., van Hagen, P. Martin, Dalm, Virgil A. S. H., IJspeert, Hanna
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7773704/
https://ncbi.nlm.nih.gov/pubmed/33391274
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.606389
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