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Toll-like receptor mediated lysozyme expression in Niemann-Pick disease, type C1

Niemann-Pick type C1 (NPC1) is a rare neurodegenerative disease. In NPC1 mouse cerebella, the antibacterial enzyme, lysozyme (Lyz2), is significantly increased in multiple cell types. Due to its possible role in toxic fibril deposition, we confirmed Lyz2 overexpression in culture in different contro...

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Dettagli Bibliografici
Pubblicato in:Mol Genet Metab
Autori principali: Cougnoux, Antony, Yerger, Julia C., Fellmeth, Mason, Serra-Vinardell, Jenny, Wassif, Christopher A., Cawley, Niamh X., Porter, Forbes D.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7736542/
https://ncbi.nlm.nih.gov/pubmed/33129690
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgme.2020.10.009
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